Type VI Constriction band syndrome
Constriction band syndrome (CBS) is a congenital disorder in which fetal parts (usually limbs or digits) are entrapped by fibrous amniotic bands while in utero. The bands form constriction rings around the digits, arms, or legs. This can result in swelling distal to the point of constriction or eventually amputation of the body part being constricted. Constriction around the digits can cause syndactyly. Constriction band syndrome is considered an accidental event.
The Amniotic Band Theory: a partial rupture of the amniotic sac causes fibrous bands to float in the amniotic fluid. The bands can encircle and trap some part or parts of the fetus. As the fetus grows, the bands do not. This constriction reduces blood circulation and natural amputations can occur before or after birth. CBS is often not seen on ultrasound imaging. In rare cases, if diagnosed in utero, amniotic band release surgery can be performed on the fetus at 28 weeks of gestation. Surgical intervention usually occurs after birth. Surgical options include: Amniotic band release, syndactyly releases, plastic and reconstructive surgeries. Staged releases are often necessary especially when multiple digits are syndactylized.
Every CBS case is unique, no two are alike.
Time to Play the Brain Game:
Q) List 3 synonyms for constriction band symdrome.
A) amniotic band syndrome (ABS), congenital constriction rings, amnion rupture sequence, limb body wall comples, streeter anomaly, streeter bands, streeter dysplasia